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ECHS1

Description enoyl-CoA hydratase, short chain 1
Image
GO Annotations Cellular Component
  • Mitochondrion
  • Mitochondrial Matrix
Molecular Function
  • Enoyl-CoA Hydratase Activity
  • Protein Binding
Biological Process
  • Fatty Acid Beta-oxidation
Pathways
  • Branched-chain amino acid catabolism
  • Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA
  • Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA
  • Beta oxidation of octanoyl-CoA to hexanoyl-CoA
  • Beta oxidation of hexanoyl-CoA to butanoyl-CoA
  • Beta oxidation of butanoyl-CoA to acetyl-CoA
Drugs
  • Hexanoyl-CoA
  • Octanoyl-Coenzyme A
  • Acetoacetyl-CoA
  • 4-(N,N-Dimethylamino)cinnamoyl-CoA
  • Omega-3-carboxylic acids
Diseases
GWAS
  • Lifespan ( 25918517)
  • Nonunion in individuals with fractures ( 30680360)
Interacting Genes 12 interacting genes: CAPN1 CBWD2 CDC42 CLDN12 CYP2E1 ERCC6 GRB2 LRRK1 LRRK2 PPM1B SERPINA1 UBA1
Entrez ID 1892
HPRD ID 03799
Ensembl ID ENSG00000127884
Uniprot IDs P30084
PDB IDs 2HW5
Enriched GO Terms of Interacting Partners?
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© Madhavi K. Ganapathiraju 2012-2025