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AARS1

Description alanyl-tRNA synthetase 1
Image
GO Annotations Cellular Component
  • Cytoplasm
  • Mitochondrion
  • Cytosol
  • Membrane
  • Extracellular Exosome
Molecular Function
  • TRNA Binding
  • Aminoacyl-tRNA Editing Activity
  • Ser-tRNA(Ala) Hydrolase Activity
  • Alanine-tRNA Ligase Activity
  • ATP Binding
  • Zinc Ion Binding
  • Amino Acid Binding
  • Translation Regulator Activity
Biological Process
  • TRNA Modification
  • TRNA Aminoacylation For Protein Translation
  • Alanyl-tRNA Aminoacylation
  • TRNA Processing
  • Cerebellar Purkinje Cell Layer Development
  • Negative Regulation Of Neuron Apoptotic Process
  • Neuromuscular Process Controlling Balance
  • Mitochondrial Alanyl-tRNA Aminoacylation
  • Aminoacyl-tRNA Metabolism Involved In Translational Fidelity
  • Regulation Of Cytoplasmic Translational Fidelity
Pathways
  • Cytosolic tRNA aminoacylation
Drugs
  • L-Alanine
Diseases
  • Charcot-Marie-Tooth disease (CMT); Hereditary motor and sensory neuropathy; Peroneal muscular atrophy
GWAS
Interacting Genes 1 interacting genes: EEF1B2
Entrez ID 16
HPRD ID 03042
Ensembl ID ENSG00000090861
Uniprot IDs P49588
PDB IDs 4XEM 4XEO 5KNN 5T5S 5T76 5V59
Enriched GO Terms of Interacting Partners?
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© Madhavi K. Ganapathiraju 2012-2025

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